Otoneurological findings prevalent in hereditary ataxias

Abstract: Objective To describe and compare the vestibular findings most evident among the hereditary ataxias, as well as correlate their clinical features with the nervous structures affected in this disease. Methods Seventy-five patients were evaluated and underwent a case history, otorhinolaryngological and vestibular assessments. Results Clinically, the patients commonly had symptoms of gait disturbances (67.1%), dizziness (47.3%), dysarthria (46%) and dysphagia (36.8%). In vestibular testing, alterations were predominantly evident in caloric testing (79%), testing for saccadic dysmetria (51%) and rotational chair testing (47%). The presence of alterations occurred in 87% of these patients. A majority of the alterations were from central vestibular dysfunction (69.3%). Conclusion This underscores the importance of the contribution of topodiagnostic labyrinthine evaluations for neurodegenerative diseases as, in most cases, the initial symptoms are otoneurological; and these evaluations should also be included in the selection of procedures to be performed in clinical and therapeutic monitoring.

Alternative title
Alteraes otoneurolgicas prevalentes nas ataxias hereditrias
Location
Deutsche Nationalbibliothek Frankfurt am Main
Extent
Online-Ressource
Language
Englisch

Bibliographic citation
Otoneurological findings prevalent in hereditary ataxias ; volume:76 ; number:03 ; year:2018 ; pages:131-138
Arquivos de neuro-psiquiatria ; 76, Heft 03 (2018), 131-138

Contributor
Zeigelboim, Bianca Simone
Teive, Hlio A. G.
Santos, Geslaine Janana Barbosa
Severiano, Maria Izabel Rodrigues
Fonseca, Vinicius Ribas
Faryniuk, Joo Henrique
Marques, Jair Mendes

DOI
10.1590/0004-282X20180001
URN
urn:nbn:de:101:1-2023101210343457044065
Rights
Open Access; Der Zugriff auf das Objekt ist unbeschränkt möglich.
Last update
14.08.2025, 11:00 AM CEST

Data provider

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Associated

  • Zeigelboim, Bianca Simone
  • Teive, Hlio A. G.
  • Santos, Geslaine Janana Barbosa
  • Severiano, Maria Izabel Rodrigues
  • Fonseca, Vinicius Ribas
  • Faryniuk, Joo Henrique
  • Marques, Jair Mendes

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