Neuromyelitis optica: phenotypic characteristics in a Brazilian case series

Objective: To describe the characteristics of 34 Brazilian NMO patients. To evaluate the contribution of the 2015 criteria to the diagnosis of NMO spectrum disorders (NMOSD) in 40 patients with longitudinal extensive transverse myelitis (LEMT). Methods: This is a retrospective, descriptive and analytic study. Results: Among NMO patients, there was a predominance of women, with onset in the fourth decade of life, and AQP4-IgG seropositivity in 73.5%. The diagnosis of NMOSD was established in 37.5% of LETM patients according to AQP4-IgG positivity and in 5% of LETM patients if the AQP4-IgG result was unknown. Conclusions: The characteristics of this series are similar to those of other Western populations. The AQP4-IgG testing assists in the diagnosis of NMOSD.

Weitere Titel
Neuromielite óptica: características fenotípicas em uma série de casos brasileiros
Standort
Deutsche Nationalbibliothek Frankfurt am Main
Umfang
Online-Ressource
Sprache
Englisch

Erschienen in
Neuromyelitis optica: phenotypic characteristics in a Brazilian case series ; volume:75 ; number:02 ; year:2017 ; pages:81-86
Arquivos de neuro-psiquiatria ; 75, Heft 02 (2017), 81-86

Beteiligte Personen und Organisationen
Del Negro, Maria Cristina
Marinho, Patricia Beatriz Christino
Papais-Alvarenga, Regina Maria

DOI
10.1590/0004-282X20160193
URN
urn:nbn:de:101:1-2023101911132953411492
Rechteinformation
Open Access; Der Zugriff auf das Objekt ist unbeschränkt möglich.
Letzte Aktualisierung
14.08.2025, 10:57 MESZ

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Beteiligte

  • Del Negro, Maria Cristina
  • Marinho, Patricia Beatriz Christino
  • Papais-Alvarenga, Regina Maria

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