TRPML1 activation ameliorates lysosomal phenotypes in CLN3 deficient retinal pigment epithelial cells

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Location: Deutsche Nationalbibliothek Frankfurt am Main

Extent: 1 Online-Ressource.

Language: Englisch

Bibliographic citation: TRPML1 activation ameliorates lysosomal phenotypes in CLN3 deficient retinal pigment epithelial cells ; volume:14 ; number:1 ; day:29 ; month:7 ; year:2024 ; pages:1-19 ; date:12.2024
Scientific reports ; 14, Heft 1 (29.7.2024), 1-19, 12.2024

Creator: Wünkhaus, D.
Tang, R.
Nyame, K.
Laqtom, N. N.
Schweizer, M.
Scotto Rosato, A.
Krogsæter, E. K.
Wollnik, C.
Abu-Remaileh, M.
Grimm, C.
Hermey, G.
Kuhn, R.
Gruber-Schoffnegger, D.
Markmann, S.

Contributor: SpringerLink (Online service)

DOI: 10.1038/s41598-024-67479-8

URN: urn:nbn:de:101:1-2410230833242.054718393698

Rights: Open Access; Der Zugriff auf das Objekt ist unbeschränkt möglich.

Last update: 15.08.2025, 7:26 AM CEST

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Associated

Wünkhaus, D.
Tang, R.
Nyame, K.
Laqtom, N. N.
Schweizer, M.
Scotto Rosato, A.
Krogsæter, E. K.
Wollnik, C.
Abu-Remaileh, M.
Grimm, C.
Hermey, G.
Kuhn, R.
Gruber-Schoffnegger, D.
Markmann, S.
SpringerLink (Online service)

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TRPML1 activation ameliorates lysosomal phenotypes in CLN3 deficient retinal pigment epithelial cells

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Other Objects (12)

Catalase-deficient mice induce aging faster through lysosomal dysfunction

Dietary restriction ameliorates TBI-induced phenotypes in Drosophila melanogaster

Combinatorial omics analysis reveals perturbed lysosomal homeostasis in collagen VII-deficient keratinocytes

D-mannose ameliorates autoimmune phenotypes in mouse models of lupus

Multi-modal proteomic characterization of lysosomal function and proteostasis in progranulin-deficient neurons

Loss of TMEM106B potentiates lysosomal and FTLD-like pathology in progranulin-deficient mice

Resveratrol ameliorates aging-related metabolic phenotypes by inhibiting cAMP phosphodiesterases

Correction: Multi-modal proteomic characterization of lysosomal function and proteostasis in progranulin-deficient neurons

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Dietary restriction ameliorates TBI-induced phenotypes in Drosophila melanogaster

Combinatorial omics analysis reveals perturbed lysosomal homeostasis in collagen VII-deficient keratinocytes

D-mannose ameliorates autoimmune phenotypes in mouse models of lupus

Multi-modal proteomic characterization of lysosomal function and proteostasis in progranulin-deficient neurons

Loss of TMEM106B potentiates lysosomal and FTLD-like pathology in progranulin-deficient mice

Resveratrol ameliorates aging-related metabolic phenotypes by inhibiting cAMP phosphodiesterases

Correction: Multi-modal proteomic characterization of lysosomal function and proteostasis in progranulin-deficient neurons

Loss of TMEM 106B potentiates lysosomal and FTLD ‐like pathology in progranulin‐deficient mice

Human VCP mutant ALS/FTD microglia display immune and lysosomal phenotypes independently of GPNMB

Knockout of secretin ameliorates biliary and liver phenotypes during alcohol-induced hepatotoxicity

Resveratrol Ameliorates Mitophagy Disturbance and Improves Cardiac Pathophysiology of Dystrophin-deficient mdx Mice

Catalase-deficient mice induce aging faster through lysosomal dysfunction

Dietary restriction ameliorates TBI-induced phenotypes in Drosophila melanogaster

Combinatorial omics analysis reveals perturbed lysosomal homeostasis in collagen VII-deficient keratinocytes

D-mannose ameliorates autoimmune phenotypes in mouse models of lupus

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Loss of TMEM106B potentiates lysosomal and FTLD-like pathology in progranulin-deficient mice

Resveratrol ameliorates aging-related metabolic phenotypes by inhibiting cAMP phosphodiesterases

Correction: Multi-modal proteomic characterization of lysosomal function and proteostasis in progranulin-deficient neurons

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Resveratrol Ameliorates Mitophagy Disturbance and Improves Cardiac Pathophysiology of Dystrophin-deficient mdx Mice

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