Giant non-functioning adrenocortical carcinoma: A rare childhood tumor

Abstract: Adrenocortical carcinoma (ACC) is a rare malignancy, especially in children. The overall incidence is approximately 2 cases per million per year. [1] In children, the incidence is 0.3 cases per million per year, except in southern Brazil where the incidence is 3.4-4.2 cases per million per year. [2] We describe a giant nonfunctioning metastasized ACC in a 6-year-old girl who presented with a history of increasing abdominal girth incidentally noticed by her mother since 1 week. Ultrasound abdomen showed a large right suprarenal tumor with calcifications and necrosis. Empty left renal fossa and compensatory enlarged right kidney were seen. Computed tomography (CT) scan revealed a large heterogenously enhancing right suprarenal mass with calcification and necrosis with pulmonary metastasis. Histopathology report from the right suprarenal mass revealed an ACC. With a stage IV disease, the patient died after 2 months from diagnosis.

Object Details

• Location: Deutsche Nationalbibliothek Frankfurt am Main
• Extent: Online-Ressource
• Language: Englisch

References and Relationships

• Bibliographic citation: Giant non-functioning adrenocortical carcinoma: A rare childhood tumor ; volume:31 ; number:02 ; year:2010 ; pages:65-68 ; Indian journal of medical & paediatric oncology ; 31, Heft 02 (2010), 65-68

Contributors, Places and Time

• Contributor: Patel, Viral V. ; Shah, Diva S. ; Raychaudhari, Chandra R. ; Patel, Keyuri B.

Further information

• DOI: 10.4103/0971-5851.71659
• URN: urn:nbn:de:101:1-2022031216395087598730
• Rights: Open Access; Der Zugriff auf das Objekt ist unbeschränkt möglich.
• Last update: 15.08.2025, 7:38 AM CEST