Neurocutaneous melanosis with hydrocephalus and dandy-walker variant
Neurocutaneous melanosis (NCM) is one of the rare, congenital, noninheritable phakomatoses characterized by the presence of large and/or multiple congenital melanocytic cutaneous nevi associated with intracranial leptomeningeal melanocytosis. NCM usually presents before 2 years of age. So far 302 cases have been reported in literature. We report a case of NCM presenting with obstructive hydrocephalus and Dandy-Walker Variant in a young adult.
- Location
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Deutsche Nationalbibliothek Frankfurt am Main
- Extent
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Online-Ressource
- Language
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Englisch
- Bibliographic citation
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Neurocutaneous melanosis with hydrocephalus and dandy-walker variant ; volume:16 ; number:04 ; year:2021 ; pages:876-880
Asian journal of neurosurgery ; 16, Heft 04 (2021), 876-880
- Contributor
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Sarwar, Mohammad
Tripathy, Laxminarayan
Jain, Harsh
Basu, Sunandan
Sengupta, Ashvini
- DOI
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10.4103/ajns.AJNS_542_20
- URN
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urn:nbn:de:101:1-2023012008561836887651
- Rights
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Open Access; Der Zugriff auf das Objekt ist unbeschränkt möglich.
- Last update
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15.08.2025, 7:31 AM CEST
Data provider
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Deutsche Nationalbibliothek. If you have any questions about the object, please contact the data provider.
Associated
- Sarwar, Mohammad
- Tripathy, Laxminarayan
- Jain, Harsh
- Basu, Sunandan
- Sengupta, Ashvini
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