The VASCERN-VASCA Working Group Diagnostic and Management Pathways for Venous Malformations

Abstract: Objective(s):
To elaborate expert consensus patient pathways to guide patients and physicians toward efficient diagnostics and management of patients with venous malformations.

Methods:
VASCERN-VASCA (https://vascern.eu/) is a European network of multidisciplinary centers for Vascular Anomalies. The Nominal Group Technique was used to establish the pathways. Two facilitators were identified: one to propose initial discussion points and draw the pathways, and another to chair the discussion. A dermatologist (AD) was chosen as first facilitator due to her specific clinical and research experience. The draft was subsequently discussed within VASCERN-VASCA monthly virtual meetings and annual face-to-face meetings.

Results:
The Pathway starts from the clinical suspicion of a venous type malformation (VM) and lists the clinical characteristics to look for to support this suspicion. Strategies for subsequent imaging and histopathology are suggested. These aim to inform on the diagnosis and to separate the patients into 4 subtypes: (1) sporadic single VMs or (2) multifocal, (3) familial, multifocal, and (4) combined and/or syndromic VMs. The management of each type is detailed in subsequent pages of the pathway, which are color coded to identify sections on (1) clinical evaluations, (2) investigations, (3) treatments, and (4) associated genes. Actions relevant to all types are marked in separate boxes, including when imaging is recommended. When definite diagnoses have been reached, the pathway also points toward disease-specific additional investigations and recommendations for follow up. Options for management are discussed for each subtype, including conservative and invasive treatments, as well as novel molecular therapies.

Conclusion:
The collaborative efforts of VASCERN-VASCA, a network of the 9 Expert Centers, has led to a consensus Diagnostic and Management Pathways for VMs to assist clinicians and patients. It also emphasizes the role of multidisciplinary expert centers in the management of VM patients. This pathway will become available on the VASCERN website (http://vascern.eu/)

Location
Deutsche Nationalbibliothek Frankfurt am Main
Extent
Online-Ressource
Language
Englisch
Notes
Journal of vascular anomalies. - 4, 2 (2023) , e064, ISSN: 2690-2702

Event
Veröffentlichung
(where)
Freiburg
(who)
Universität
(when)
2023
Creator
Dompmartin, Anne
Baselga Torres, Eulalia
Boon, Laurence M.
Diociaiuti, Andrea
Dvorakova, Veronika
El Hachem, Maya
Gasparella, Paolo
Haxhija, Emir Q.
Ghaffarpour, Nader
Kyrklund, Kristiina
Irvine, Alan
Kapp, Friedrich
Rößler, Jochen
Salminen, Päivi
Bosch, Caroline van den
Vleuten, Carine van der
Schultze Kool, Leo
Vikkula, Miikka

DOI
10.1097/jova.0000000000000064
URN
urn:nbn:de:bsz:25-freidok-2373819
Rights
Open Access; Der Zugriff auf das Objekt ist unbeschränkt möglich.
Last update
25.03.2025, 1:47 PM CET

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Associated

  • Dompmartin, Anne
  • Baselga Torres, Eulalia
  • Boon, Laurence M.
  • Diociaiuti, Andrea
  • Dvorakova, Veronika
  • El Hachem, Maya
  • Gasparella, Paolo
  • Haxhija, Emir Q.
  • Ghaffarpour, Nader
  • Kyrklund, Kristiina
  • Irvine, Alan
  • Kapp, Friedrich
  • Rößler, Jochen
  • Salminen, Päivi
  • Bosch, Caroline van den
  • Vleuten, Carine van der
  • Schultze Kool, Leo
  • Vikkula, Miikka
  • Universität

Time of origin

  • 2023

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