Rare Cause of Secondary Pulmonary Arterial Hypertension

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Abstract: Unilateral absent pulmonary artery (UAPA) is a rare congenital disorder. Most of the patients will be diagnosed in the early childhood because of recurrent respiratory tract infections and hemoptysis, but adult presentation is not uncommon. We report a 47-year-old female who was earlier diagnosed as bronchiectasis with pulmonary artery hypertension but now presented with complaints of typical angina and dyspnea on exertion. During right heart catheterization we failed to enter right pulmonary artery (RPA), and conventional coronary angiogram showed a large left atrial branch of left circumflex giving collateral blood supply to the right lung. Computed tomography angiogram showed absent RPA. We report this case not only because the patient was misdiagnosed but also because of rarity of coronary collaterals in UAPA patients and unusual bilateral bronchiectasis. According to reported literature, ours is the 28th case of this nature.

Location: Deutsche Nationalbibliothek Frankfurt am Main

Extent: Online-Ressource

Language: Englisch

Bibliographic citation: Rare Cause of Secondary Pulmonary Arterial Hypertension ; day:21 ; month:04 ; year:2022
Indian Journal of Cardiovascular Disease in Women WINCARS ; (21.04.2022)

Contributor: Pasula, Anand Yadav
Karthikeya, Kapil
Patnaik, Sujata
Howdekar, Madhuri

DOI: 10.1055/s-0041-1740355

URN: urn:nbn:de:101:1-2022060911243539786974

Rights: Open Access; Der Zugriff auf das Objekt ist unbeschränkt möglich.

Last update: 15.08.2025, 7:22 AM CEST

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Pasula, Anand Yadav
Karthikeya, Kapil
Patnaik, Sujata
Howdekar, Madhuri

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Rare Cause of Secondary Pulmonary Arterial Hypertension

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Other Objects (12)

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