ATRT of lateral ventricle in a child: A rare tumor at a very rare location
Atypical teratoid/rhabdoid tumors (AT/RTs) of infancy are highly malignant central nervous system neoplasms that are most commonly seen during the first 2 years of life with limited therapeutic options. To date, only two cases have been described in the lateral ventricle. A 4-year-old boy presented with a 4-month history of increased intracranial pressure. Cerebral magnetic resonance imaging (MRI) revealed a huge intraventricular tumor, occupying the entire temporal horn and the body of the left lateral ventricle. The boy was operated through a left temporal transventricular approach with gross total removal of the lesion. The histopathological diagnosis was an AT/RT. The infant underwent adjuvant chemotherapy and radiation therapy. The 1-year MRI of control showed a local recurrence of the tumor. Then after, Gamma Knife radiosurgery was performed because of the small volume and the deep location of the lesion. At the 3-month follow-up, the MRI showed a significant growth of the tumor volume, and the child was given additional adjuvant chemotherapy. Unfortunately, he died 9 months later. AT/RT of the lateral ventricle is a very rare tumor in children, associated with a poor prognosis in spite of multimodal treatment. Gamma knife surgery (GKS) was rarely reported as a treatment modality of AT/RT. The aim of this work is to discuss about the rarity of this tumor and the best treatment strategy to improve prognosis.
- Location
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Deutsche Nationalbibliothek Frankfurt am Main
- Extent
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Online-Ressource
- Language
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Englisch
- Bibliographic citation
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ATRT of lateral ventricle in a child: A rare tumor at a very rare location ; volume:15 ; number:01 ; year:2020 ; pages:225-229
Asian journal of neurosurgery ; 15, Heft 01 (2020), 225-229
- Contributor
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Lakhdar, Fayçal
Benzagmout, Mohammed
Arkha, Yasser
Chakour, Khalid
Chaoui, Mohammed
- DOI
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10.4103/ajns.AJNS_128_19
- URN
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urn:nbn:de:101:1-2023011916035385695547
- Rights
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Open Access; Der Zugriff auf das Objekt ist unbeschränkt möglich.
- Last update
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15.08.2025, 7:30 AM CEST
Data provider
Deutsche Nationalbibliothek. If you have any questions about the object, please contact the data provider.
Associated
- Lakhdar, Fayçal
- Benzagmout, Mohammed
- Arkha, Yasser
- Chakour, Khalid
- Chaoui, Mohammed