Isolated intraventricular Rosai–Dorfman disease
Rosai–Dorfman disease (RDD) is a benign histioproliferative disorder characterized by generalized lymphadenopathy, weakness, anemia, and rarely extranodal involvement. The disease affects the central nervous system (CNS) very rarely and at a relatively older age. Isolated intracranial involvement is very rare. RDD tends to present as dural masses mimicking meningioma, though very rare case reports describe isolated parenchymal involvement in the CNS. Only one case of intraventricular RDD has been described so far to the best of our knowledge. We present a very rare presentation of this disease as an isolated intraventricular presentation in the region of the atria of the lateral ventricles.
- Standort
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Deutsche Nationalbibliothek Frankfurt am Main
- Umfang
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Online-Ressource
- Sprache
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Englisch
- Erschienen in
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Isolated intraventricular Rosai–Dorfman disease ; volume:13 ; number:04 ; year:2018 ; pages:1285-1287
Asian journal of neurosurgery ; 13, Heft 04 (2018), 1285-1287
- Beteiligte Personen und Organisationen
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Patwardhan, Pranav
Goel, Naina
- DOI
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10.4103/ajns.AJNS_134_18
- URN
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urn:nbn:de:101:1-2022112410361036586306
- Rechteinformation
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Open Access; Der Zugriff auf das Objekt ist unbeschränkt möglich.
- Letzte Aktualisierung
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15.08.2025, 07:23 MESZ
Datenpartner
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Beteiligte
- Patwardhan, Pranav
- Goel, Naina